Response to Disodium Etidronate Treatment in Three Siblings with Pulmonary Alveolar Microlithiasis
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چکیده
منابع مشابه
Response to Disodium Etidronate Treatment in Three Siblings with Pulmonary Alveolar Microlithiasis.
Pulmonary alveolar microlithiasis (PAM) is a rare chronic genetic lung disease in childhood with no proven therapy. It is characterized by the deposition of calcium phosphate microliths within the alveolar air spaces. The effect of disodium etidronate (DE) treatment on PAM is controversial. We report 3 siblings (an 11-year-old boy and 4-year-old twin girls) with PAM diagnosed by chest X-ray, th...
متن کاملFamilial occurrence of pulmonary alveolar microlithiasis in 3 siblings.
Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology characterized by intra-alveolar calcium deposits. More than 500 cases were reported in the literature. The disorder affects people at every age beginning from the early childhood. It occurs probably as a result of autosomal recessive transmission. Familial occurrence is often found with family history of the disease b...
متن کاملPulmonary Alveolar Microlithiasis: A Rare Case Report
Pulmonary alveolar microlithiasis is an uncommon infiltrative pulmonary disease characterized by deposition of microliths in the alveoli. We present the case of a young adult with complaints of shortness of breath on exertion. Chest radiograph showed innumerable small, dense nodules, diffusely involving both the lungs - predominantly in the lower zones. High-resolution CT scan illustrated wides...
متن کاملA Case Report of Pulmonary Alveolar Microlithiasis
Pulmonary alveolar microlithiasis is a rare autosomal recessive disease characterized by the formation of calcium phosphate deposition in the alveoli. Although the disease most often occurs in children, most patients with the disease are diagnosed in adulthood due to the slow progression of the disease inside the lungs. In childhood, it often causes no symptoms, and changes in the lung parenchy...
متن کامل[Pulmonary alveolar microlithiasis].
The authors present two of their own observations where, based on the clinical course of the disease and the X-ray finding, they diagnosed the condition as pulmonary alveolar microlithiasis. They present a review of the literature as regards new views on the pathogenesis, diagnosis and therapy of the condition. They evaluate the contribution of scintigraphy 99 mTc, bronchial lavage and X-ray me...
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ژورنال
عنوان ژورنال: Respiration
سال: 2015
ISSN: 0025-7931,1423-0356
DOI: 10.1159/000375464